{"doi":"10.5414/np300395","title":"Non-necrotizing autoimmune myopathy with pipestem type capillaries – a light and electron microscopic study","abstract":null,"journal":"Clinical Neuropathology","year":2012,"id":688193,"datarank":0.29188652235829704,"base_score":1.9459101490553132,"endowment":1.9459101490553132,"self_citation_contribution":0.29188652235829704,"citation_network_contribution":0.0,"self_endowment_contribution":0.29188652235829704,"citer_contribution":0.0,"corpus_percentile":null,"corpus_rank":null,"citation_count":6,"citer_count":0,"citers_with_citation_signal":0,"citers_with_endowment":0,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":null,"is_data_producer":false,"deposit_databanks":null,"is_oa":false,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":null,"fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":316895,"name":"Michael Weber","orcid":"0000-0002-8507-2219","position":1,"is_corresponding":false},{"id":1797837,"name":"Wolfgang Schlote","orcid":null,"position":2,"is_corresponding":false},{"id":1797836,"name":"Rudolf Wilhelm Christian Janzen","orcid":null,"position":0,"is_corresponding":false}],"reference_count":0,"raw_metadata":{"has_enrichment":true,"resolved":true,"title":"Non-necrotizing autoimmune myopathy with pipestem type capillaries – a light and electron microscopic study","abstract":"We report on 7 cases of a nonnecrotizing type of autoimmune myopathy found in suspected connective tissue disease and related disorders. In muscle biopsy, these cases showed myopathic alterations characterized by irregular outlines of muscle fibers in cross and longitudinal section nearly or totally lacking inflammatory cell infiltrations or macrophages and no necroses of myofibers. They revealed deposition of immunoglobulins and of collagen IV antibodies attached to fiber surface. The number of capillaries per myofiber was enlarged. Capillaries of pipestem type with thickened wall were found at the electron microscopic level. This type of myopathy was seen especially in subacute cases presenting with muscle pain, weakness and increased unspecific inflammatory laboratory parameters. No evidence for polymyositis, dermatomyositis or inclusion body myositis could be found. In all cases, steroid therapy was of striking benefit.","is_dataset_classified":null,"base_score":1.9459101490553132,"endowment":1.9459101490553132,"datacite_reuse_total":0,"file_count":0,"downloads":0,"views":0,"has_version_chain":false,"is_dataset":false,"is_oa":false,"pmid":"22385789","pmcid":null,"openalex_id":"https://openalex.org/W2313411122","authors":[],"funders":[],"total_grants":0,"fwci":0.8145,"citation_percentile":0.7515169,"influential_citations":0,"citation_trend":[{"year":2012,"count":2},{"year":2013,"count":2},{"year":2022,"count":1},{"year":2024,"count":1}],"oa_status":"closed","license":null,"oa_locations":[{"url":"https://doi.org/10.5414/np300395","host_type":"journal"},{"url":"https://pubmed.ncbi.nlm.nih.gov/22385789","host_type":"repository"}],"fields_of_study":["Inflammatory Myopathies and Dermatomyositis","Parkinson's Disease and Spinal Disorders","Genetic Neurodegenerative Diseases","Adult","Aged","Aged, 80 and over","Autoimmune Diseases","Capillaries","Connective Tissue Diseases","Female","Humans","Male","Middle Aged","Muscle, Skeletal","Muscular Diseases","Myositis"],"mesh_terms":["Adult","Aged","Aged, 80 and over","Autoimmune Diseases","Capillaries","Connective Tissue Diseases","Female","Humans","Male","Middle Aged","Muscular Diseases","Myositis","Muscle, Skeletal"],"keywords":["Polymyositis","Dermatomyositis","Pathology","Inclusion body myositis","Muscle biopsy","Inflammatory myopathy","Medicine","Myopathy","Connective tissue","Myositis","Myocyte","Biopsy","Proximal muscle weakness","Connective tissue disease","Endomysium","Autoimmune disease","Disease","Internal medicine"],"sdg_mappings":[{"sdg_number":0,"sdg_label":"Good health and well-being"}],"linked_datasets":[],"clinical_trials":[],"software_tools":[],"database_accessions":[],"source":"live","citation_network_status":"fetched"},"created_at":"2026-08-19T13:54:57.892520Z","pmid":null,"pmcid":null,"fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}