{"doi":"10.4111/kju.2007.48.3.344","title":"Spontaneous Rupture of Renal Angiomyolipoma in a Female Tuberous Sclerosis Patient with Pulmonary Lymphangioleiomyomatosis","abstract":null,"journal":"Korean Journal of Urology","year":2007,"id":677072,"datarank":0.10397207708399181,"base_score":0.6931471805599453,"endowment":0.6931471805599453,"self_citation_contribution":0.10397207708399181,"citation_network_contribution":0.0,"self_endowment_contribution":0.10397207708399181,"citer_contribution":0.0,"corpus_percentile":null,"corpus_rank":null,"citation_count":1,"citer_count":0,"citers_with_citation_signal":0,"citers_with_endowment":0,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":null,"is_data_producer":false,"deposit_databanks":null,"is_oa":false,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":null,"fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":1769078,"name":"Tae Won Lee","orcid":null,"position":1,"is_corresponding":false},{"id":1769079,"name":"Myung Joon Kim","orcid":null,"position":2,"is_corresponding":false},{"id":1769080,"name":"Mi Mi Oh","orcid":null,"position":3,"is_corresponding":false},{"id":733963,"name":"Jae Hyun Bae","orcid":"0000-0002-1384-6123","position":4,"is_corresponding":false},{"id":1769081,"name":"Hong Seok Park","orcid":null,"position":5,"is_corresponding":false},{"id":1769082,"name":"Je Jong Kim","orcid":null,"position":6,"is_corresponding":false},{"id":1769084,"name":"Kang Soo Shim","orcid":null,"position":7,"is_corresponding":false},{"id":1017416,"name":"Jong Wook Kim","orcid":null,"position":0,"is_corresponding":false}],"reference_count":0,"raw_metadata":{"has_enrichment":true,"resolved":true,"title":"Spontaneous Rupture of Renal Angiomyolipoma in a Female Tuberous Sclerosis Patient with Pulmonary Lymphangioleiomyomatosis","abstract":"결절성 경화증 (tuberous sclerosis; TS)은 드문 상염색체 우 성 유전질환으로 경련이나 피부병변 또는 다양한 장기의 과오종성 병변을 일으킨다. TS 환자에서 가장 흔하게 발견 되는 신장 병변은 신혈관근지방종 (angiomyolipoma; AML) 으로 약 40-80%를 차지하고 다발성이나 양측성으로 나타나 는 경우가 많다. 1 호흡기 림프관근종증 (lymphangioleiomyomatosis; LAM)은 혈관 주변, 림프관 주변, 폐포벽, 기관지 주변 평활근의 과오종성 증식을 특징으로 하는 드문 증식 성 질환이다. TS가 아닌 경우에 AML은 LAM이 있는 환자 에서 30-60% 정도에서 발견되며 LAM이 진단되기 수 년 전 에 발생하는 경우도 많은 것으로 보고되고 있다. 2 이런 경 우, 호흡기 LAM은 HMB-45에 양성을 보이는 평활근의 과 오종성 증식으로 특징지어지며, AML과의 연관성에 대해서 는 아직 잘 알려져 있지 않으나 호르몬 환경이 중요한 인자 인 것으로 보고되고 있다. 3","is_dataset_classified":null,"base_score":0.6931471805599453,"endowment":0.6931471805599453,"datacite_reuse_total":0,"file_count":0,"downloads":0,"views":0,"has_version_chain":false,"is_dataset":false,"is_oa":false,"pmid":"26207759","pmcid":null,"openalex_id":"https://openalex.org/W2062238845","authors":[],"funders":[],"total_grants":0,"fwci":0.1632,"citation_percentile":0.55084794,"influential_citations":0,"citation_trend":[],"oa_status":"closed","license":"http://creativecommons.org/licenses/by-nc/3.0/","oa_locations":[{"url":"https://synapse.koreamed.org/DOIx.php?id=10.4111/kju.2007.48.3.344","host_type":"publisher"},{"url":"https://synapse.koreamed.org/pdf/10.4111/kju.2007.48.3.344","host_type":"publisher"},{"url":"https://icurology.org/DOIx.php?id=10.4111/kju.2007.48.3.344","host_type":"publisher"},{"url":"https://doi.org/10.4111/kju.2007.48.3.344","host_type":"journal"}],"fields_of_study":["Tuberous Sclerosis Complex Research"],"mesh_terms":[],"keywords":["Tuberous sclerosis","Lymphangioleiomyomatosis","Angiomyolipoma","Medicine","Internal medicine","Pathology","Kidney"],"sdg_mappings":[{"sdg_number":0,"sdg_label":"Good health and well-being"}],"linked_datasets":[],"clinical_trials":[],"software_tools":[],"database_accessions":[],"source":"live","citation_network_status":"fetched"},"created_at":"2026-08-17T03:35:08.360403Z","pmid":null,"pmcid":null,"fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}