{"doi":"10.1177/003335491613100221","title":"Defining Sickle Cell Disease Mortality Using a Population-Based Surveillance System, 2004 through 2008","abstract":"<jats:sec>\n                    <jats:title>Objective.</jats:title>\n                    <jats:p>Population-based surveillance data from California and Georgia for years 2004 through 2008 were linked to state death record files to determine the all-cause death rate among 12,143 patients identified with sickle cell disease (SCD).</jats:p>\n                  </jats:sec>\n                  <jats:sec>\n                    <jats:title>Methods.</jats:title>\n                    <jats:p>All-cause death rates, by age, among these SCD patients were compared with all-cause death rates among both African Americans and the total population in the two states. All-cause death rates were also compared with death rates for SCD derived from publicly available death records: the compressed mortality files and multiple cause of death files.</jats:p>\n                  </jats:sec>\n                  <jats:sec>\n                    <jats:title>Results.</jats:title>\n                    <jats:p>Of 12,143 patients identified with SCD, 615 patients died. The all-cause mortality rate for the SCD population was lower than the all-cause mortality rate among African Americans and similar to the total population all-cause mortality rates from birth through age 4 years, but the rate was higher among those with SCD than both the African American and total population rates from ages 5 through 74 years. The count of deceased patients identified by using population-based surveillance data ( n=5615) was more than twice as high as the count identified in compressed mortality files using SCD as the underlying cause of death alone ( n=5297).</jats:p>\n                  </jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion.</jats:title>\n                    <jats:p>Accurate assessment of all-cause mortality and age at death requires long-term surveillance via population-based registries of patients with accurately diagnosed SCD.</jats:p>\n                  </jats:sec>","journal":"Public Health Reports®","year":2016,"id":13662,"datarank":3.9813207096959538,"base_score":4.51085950651685,"endowment":4.51085950651685,"self_citation_contribution":0.6766289259775276,"citation_network_contribution":3.304691783718426,"self_endowment_contribution":0.6766289259775276,"citer_contribution":3.304691783718426,"corpus_percentile":69.9,"corpus_rank":374,"citation_count":90,"citer_count":76,"citers_with_citation_signal":60,"citers_with_endowment":60,"datacite_reuse_total":0,"is_dataset":true,"is_dataset_confidence":null,"is_oa":false,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":null,"fair_score":36.6667,"fair_percentile":18.38170624450308,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":111159,"name":"James R. Eckman","orcid":null,"position":1,"is_corresponding":false},{"id":111160,"name":"Angela B. Snyder","orcid":null,"position":2,"is_corresponding":false},{"id":111161,"name":"Ward Hagar","orcid":null,"position":3,"is_corresponding":false},{"id":111162,"name":"Lisa B. Feuchtbaum","orcid":null,"position":4,"is_corresponding":false},{"id":45454,"name":"Mei Zhou","orcid":"0000-0002-8510-5287","position":5,"is_corresponding":false},{"id":111163,"name":"Althea M. Grant","orcid":null,"position":6,"is_corresponding":false},{"id":111164,"name":"Mary M. Hulihan","orcid":null,"position":7,"is_corresponding":false},{"id":111158,"name":"Susan T. Paulukonis","orcid":null,"position":0,"is_corresponding":false}],"reference_count":0,"raw_metadata":{"has_enrichment":true,"base_score":4.51085950651685,"endowment":4.51085950651685,"datacite_reuse_total":0,"file_count":0,"downloads":0,"views":0,"has_version_chain":false,"is_dataset":false,"is_oa":false,"pmid":"26957672","pmcid":"PMC4765986","openalex_id":"https://openalex.org/W2473332645","authors":[],"funders":[],"total_grants":0,"fwci":4.5683,"citation_percentile":0.95205318,"influential_citations":6,"citation_trend":[{"year":2016,"count":2},{"year":2017,"count":8},{"year":2018,"count":4},{"year":2019,"count":9},{"year":2020,"count":14},{"year":2021,"count":7},{"year":2022,"count":10},{"year":2023,"count":17},{"year":2024,"count":7},{"year":2025,"count":9},{"year":2026,"count":3}],"oa_status":"bronze","license":"https://journals.sagepub.com/page/policies/text-and-data-mining-license","oa_locations":[{"url":"https://journals.sagepub.com/doi/pdf/10.1177/003335491613100221","host_type":"journal"},{"url":"https://journals.sagepub.com/doi/pdf/10.1177/003335491613100221","host_type":"BRONZE"},{"url":"https://journals.sagepub.com/doi/pdf/10.1177/003335491613100221","host_type":"publisher"},{"url":"https://doi.org/10.1177/003335491613100221","host_type":"journal"},{"url":"https://pubmed.ncbi.nlm.nih.gov/26957672","host_type":"repository"},{"url":"https://scholarworks.gsu.edu/ghpc_articles/3","host_type":"repository"},{"url":"https://scholarworks.gsu.edu/cgi/viewcontent.cgi?article=1175&context=ghpc_articles","host_type":"repository"},{"url":"https://www.ncbi.nlm.nih.gov/pmc/articles/4765986","host_type":"repository"},{"url":"https://hdl.handle.net/20.500.14694/6758","host_type":"repository"}],"fields_of_study":["Hemoglobinopathies and Related Disorders","Blood groups and transfusion","Organ Donation and Transplantation","Medicine","Adolescent","Adult","Black or African American","Age Distribution","Aged","Anemia, Sickle Cell","California","Cause of Death","Child","Child, Preschool","Death Certificates","Female","Georgia","Humans","Infant","Infant, Newborn","Male","Medical Record Linkage","Middle Aged","Neonatal Screening","Population Surveillance","Sex Distribution","Young Adult"],"mesh_terms":["Adolescent","Adult","Aged","Anemia, Sickle Cell","Black or African American","California","Cause of Death","Child","Child, Preschool","Death Certificates","Female","Georgia","Humans","Infant","Infant, Newborn","Male","Medical Record Linkage","Middle Aged","Population Surveillance","Neonatal Screening","Age Distribution","Sex Distribution","Young Adult"],"keywords":["Population","Disease","Disease surveillance","Medicine","Environmental health","Demography","Pathology"],"sdg_mappings":[{"sdg_number":0,"sdg_label":"Good health and well-being"}],"linked_datasets":[],"clinical_trials":[],"software_tools":[],"database_accessions":[],"source":"live","citation_network_status":"fetched"},"created_at":"2026-05-31T08:48:44.289502Z","pmid":"26957672","pmcid":"PMC4765986","fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":69.0,"fair_a":56.0,"fair_i":5.0,"fair_r":16.6667,"fair_zscore":-0.7729,"fair_rationale":{"fair_score":36.67,"has_llm":true,"dimensions":{"F":{"name":"Findable","score":69.0,"criteria":[{"key":"f_has_doi","label":"Has a persistent DOI","kind":"deterministic","weight":1.0,"fraction":1.0,"signal":"DOI present","rationale":null},{"key":"f_repository_presence","label":"Indexed in repositories / literature DBs","kind":"deterministic","weight":1.0,"fraction":1.0,"signal":"datacite=0, pmcid=True, pmid=True","rationale":null},{"key":"f_persistent_ids","label":"Resolvable scholarly identifiers (OpenAlex)","kind":"deterministic","weight":0.5,"fraction":0.0,"signal":"no OpenAlex id","rationale":null},{"key":"f_metadata_richness","label":"Rich, machine-readable metadata","kind":"llm","weight":1.0,"fraction":0.25,"signal":null,"rationale":"The paper states use of surveillance data linked to state death records and mentions specific years (2004-2008), but provides no machine-readable metadata, data dictionary, or structured description of the dataset."}]},"A":{"name":"Accessible","score":56.0,"criteria":[{"key":"a_open_access","label":"Open Access / files deposited","kind":"deterministic","weight":1.5,"fraction":0.5,"signal":"files/OA location present but not flagged OA","rationale":null},{"key":"a_retrievable","label":"Free full text retrievable","kind":"deterministic","weight":1.0,"fraction":1.0,"signal":"9 OA location(s)","rationale":null},{"key":"a_access_protocol","label":"Clear data/code access protocol","kind":"llm","weight":1.0,"fraction":0.0,"signal":null,"rationale":"No access protocol, repository link, or contact information is provided for obtaining the data or code; 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