{"doi":"10.1159/000486932","title":"New Insights into Cystic Kidney Diseases","abstract":null,"journal":"Contributions to Nephrology","year":2018,"id":644304,"datarank":0.6705679643006424,"base_score":2.1972245773362196,"endowment":2.1972245773362196,"self_citation_contribution":0.32958368660043297,"citation_network_contribution":0.34098427770020945,"self_endowment_contribution":0.32958368660043297,"citer_contribution":0.34098427770020945,"corpus_percentile":null,"corpus_rank":null,"citation_count":8,"citer_count":8,"citers_with_citation_signal":6,"citers_with_endowment":6,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":null,"is_data_producer":false,"deposit_databanks":null,"is_oa":false,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":null,"fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":1669245,"name":"Shiho Makabe","orcid":null,"position":1,"is_corresponding":false},{"id":161151,"name":"Yumi Aoyama","orcid":null,"position":2,"is_corresponding":false},{"id":288850,"name":"Hiroshi Kataoka","orcid":"0000-0002-2502-8304","position":3,"is_corresponding":false},{"id":1667792,"name":"Kosaku Nitta","orcid":"0000-0002-9548-054X","position":4,"is_corresponding":false},{"id":1669251,"name":"Toshio Mochizuki","orcid":"0000-0002-3820-3191","position":0,"is_corresponding":false}],"reference_count":0,"raw_metadata":{"has_enrichment":true,"resolved":true,"title":"New Insights into Cystic Kidney Diseases","abstract":"Hereditary cystic kidney diseases are considered as \"ciliopathies\" caused by abnormalities of the \"primary cilia\" situated on the tubules. As a result of dysplasia and dysfunction of cilia, formation of cysts occurs at various stages of life. Although occurring at a low incidence, hereditary cystic kidney diseases that develop from the fetal stage to childhood are diverse and are often associated with systemic disorders. The incidence of autosomal dominant polycystic kidney disease, which is the only adult-onset hereditary cystic kidney disease, is the highest among hereditary renal disorders.","is_dataset_classified":null,"base_score":2.1972245773362196,"endowment":2.1972245773362196,"datacite_reuse_total":0,"file_count":0,"downloads":0,"views":0,"has_version_chain":false,"is_dataset":false,"is_oa":false,"pmid":"29734148","pmcid":null,"openalex_id":"https://openalex.org/W2800640234","authors":[],"funders":[],"total_grants":0,"fwci":6.6329,"citation_percentile":0.96186823,"influential_citations":0,"citation_trend":[{"year":2020,"count":4},{"year":2021,"count":2},{"year":2022,"count":1},{"year":2023,"count":1}],"oa_status":"closed","license":"https://www.karger.com/Services/SiteLicenses","oa_locations":[{"url":"https://www.karger.com/Article/Pdf/486932","host_type":"publisher"},{"url":"https://doi.org/10.1159/000486932","host_type":"book series"},{"url":"https://pubmed.ncbi.nlm.nih.gov/29734148","host_type":"repository"}],"fields_of_study":["Genetic and Kidney Cyst Diseases","Biomedical Research and Pathophysiology","Renal and related cancers","Abnormalities, Multiple","Anemia","Bardet-Biedl Syndrome","Cerebellum","Ciliary Motility Disorders","Ciliopathies","Encephalocele","Eye Abnormalities","Humans","Hyperuricemia","Kidney Diseases, Cystic","Leber Congenital Amaurosis","Optic Atrophies, Hereditary","Orofaciodigital Syndromes","Polycystic Kidney Diseases","Polycystic Kidney, Autosomal Dominant","Polycystic Kidney, Autosomal Recessive","Renal Insufficiency","Renin","Retina","Retinitis Pigmentosa","Uromodulin","Agenesis of Cerebellar Vermis","Hyperuricemic Nephropathy, Familial Juvenile 2","Meckel syndrome type 1","Medullary Cystic Kidney Disease 2","Medullary cystic kidney disease 1","Nephronophthisis 2","Nephronophthisis 3","Nephronophthisis 4","Senior Loken Syndrome"],"mesh_terms":["Abnormalities, Multiple","Ciliopathies","Anemia","Cerebellum","Ciliary Motility Disorders","Encephalocele","Eye Abnormalities","Humans","Polycystic Kidney Diseases","Orofaciodigital Syndromes","Renin","Retina","Retinitis Pigmentosa","Optic Atrophies, Hereditary","Polycystic Kidney, Autosomal Dominant","Polycystic Kidney, Autosomal Recessive","Bardet-Biedl Syndrome","Hyperuricemia","Renal Insufficiency","Kidney Diseases, Cystic","Leber Congenital Amaurosis","Uromodulin"],"keywords":["Cilium","Ciliopathies","Medicine","Autosomal Recessive Polycystic Kidney Disease","Nephronophthisis","Cystic kidney disease","Polycystic kidney disease","Kidney","Pathology","Disease","Incidence (geometry)","Dysplasia","Internal medicine","Biology","Genetics","Phenotype"],"sdg_mappings":[{"sdg_number":0,"sdg_label":"Good health and well-being"}],"linked_datasets":[],"clinical_trials":[],"software_tools":[],"database_accessions":[],"source":"live","citation_network_status":"fetched"},"created_at":"2026-08-09T00:51:49.029424Z","pmid":null,"pmcid":null,"fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}