{"doi":"10.1152/ajpheart.00601.2023","title":"Increased heart rate fragmentation in those with Williams–Beuren syndrome suggests nonautonomic mechanistic contributors to sudden death risk","abstract":"This work is the first to apply heart rate fragmentation analyses to individuals with Williams syndrome and posits that the heart rate fragmentation parameter W 3 may enable detection and investigation of phenomena underlying the proarrhythmic short-long-short RR interval sequences paradigm known to precede ventricular fibrillation and ventricular tachycardia. It also forwards a novel method for quantifying sinus arrhythmia and sinus pauses that likely correlate with parasympathetic activity.","journal":"American Journal of Physiology-Heart and Circulatory Physiology","year":2024,"id":471266,"datarank":0.0,"base_score":0.0,"endowment":0.0,"self_citation_contribution":0.0,"citation_network_contribution":0.0,"self_endowment_contribution":0.0,"citer_contribution":0.0,"corpus_percentile":null,"corpus_rank":null,"citation_count":2,"citer_count":0,"citers_with_citation_signal":0,"citers_with_endowment":0,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":0.9575,"is_data_producer":false,"deposit_databanks":null,"is_oa":false,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":"2024-01-01","fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":1305826,"name":"Anna Bellach","orcid":"0000-0002-3476-0097","position":1,"is_corresponding":false},{"id":360928,"name":"James Troendle","orcid":"0000-0002-7903-1015","position":2,"is_corresponding":false},{"id":94201,"name":"Kevin M. Smith","orcid":"0000-0002-6736-4779","position":3,"is_corresponding":false},{"id":879820,"name":"Sharon Osgood","orcid":"0000-0002-1080-9212","position":4,"is_corresponding":false},{"id":880332,"name":"Neelam Raja","orcid":null,"position":5,"is_corresponding":false},{"id":337303,"name":"Beth A. Kozel","orcid":"0000-0002-9757-7118","position":6,"is_corresponding":false},{"id":447523,"name":"Mark Levin","orcid":"0000-0002-2241-9828","position":7,"is_corresponding":false},{"id":953325,"name":"Brianna Cathey","orcid":"0000-0003-2691-6669","position":0,"is_corresponding":true}],"reference_count":55,"raw_metadata":null,"created_at":"2026-07-19T02:05:44.736405Z","pmid":"38904853","pmcid":null,"fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}