{"doi":"10.1111/j.1460-9592.1992.tb00193.x","title":"Caudal anaesthesia in a patient with Hurler syndrome (mucopolysaccharidosis type I)","abstract":"<jats:title>Summary</jats:title><jats:p>Children with any of the mucopolysaccharidoses are at a high risk of developing significant morbidity and mortality when a general anaesthetic is administered. This case report describes the use of a caudal epidural technique for the repair of bilateral inguinal herniae in a 10‐month‐old infant with Hurler syndrome (mucopolysaccharidosis type I).</jats:p>","journal":"Pediatric Anesthesia","year":1992,"id":15563,"datarank":0.16479184330021646,"base_score":1.0986122886681096,"endowment":1.0986122886681096,"self_citation_contribution":0.16479184330021646,"citation_network_contribution":0.0,"self_endowment_contribution":0.16479184330021646,"citer_contribution":0.0,"corpus_percentile":null,"corpus_rank":null,"citation_count":2,"citer_count":2,"citers_with_citation_signal":0,"citers_with_endowment":0,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":null,"is_oa":false,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":null,"fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":118361,"name":"P.G. COLES","orcid":null,"position":1,"is_corresponding":false},{"id":118360,"name":"E.J. WALBERGH","orcid":null,"position":0,"is_corresponding":false}],"reference_count":0,"raw_metadata":{"has_enrichment":true,"base_score":1.0986122886681096,"endowment":1.0986122886681096,"datacite_reuse_total":0,"file_count":0,"downloads":0,"views":0,"has_version_chain":false,"is_dataset":false,"is_oa":false,"pmid":"21071399","pmcid":null,"openalex_id":"https://openalex.org/W2114121875","authors":[],"funders":[],"total_grants":0,"fwci":0.0,"citation_percentile":0.16107835,"influential_citations":0,"citation_trend":[],"oa_status":"closed","license":"http://onlinelibrary.wiley.com/termsAndConditions#vor","oa_locations":[{"url":"https://api.wiley.com/onlinelibrary/tdm/v1/articles/10.1111%2Fj.1460-9592.1992.tb00193.x","host_type":"publisher"},{"url":"https://onlinelibrary.wiley.com/doi/pdf/10.1111/j.1460-9592.1992.tb00193.x","host_type":"publisher"},{"url":"https://doi.org/10.1111/j.1460-9592.1992.tb00193.x","host_type":"journal"}],"fields_of_study":["Lysosomal Storage Disorders Research","Intestinal and Peritoneal Adhesions","Child Nutrition and Feeding Issues","Medicine"],"mesh_terms":[],"keywords":["Medicine","Hurler syndrome","Mucopolysaccharidosis","Mucopolysaccharidosis type I","Mucopolysaccharidosis I","Hunter syndrome","General anaesthesia","Surgery","Anesthesia","Pediatrics","Disease","Internal medicine","Enzyme replacement therapy"],"sdg_mappings":[{"sdg_number":0,"sdg_label":"Good health and well-being"}],"linked_datasets":[],"clinical_trials":[],"software_tools":[],"database_accessions":[],"source":"live","citation_network_status":"fetched"},"created_at":"2026-06-01T18:12:20.347406Z","pmid":null,"pmcid":null,"fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}