{"doi":"10.1016/j.jdcr.2020.05.015","title":"A case of congenital dermatofibrosarcoma protuberans in a 2-year-old child","abstract":null,"journal":"JAAD Case Reports","year":2020,"id":614322,"datarank":0.24141568686511508,"base_score":1.6094379124341003,"endowment":1.6094379124341003,"self_citation_contribution":0.24141568686511508,"citation_network_contribution":0.0,"self_endowment_contribution":0.24141568686511508,"citer_contribution":0.0,"corpus_percentile":null,"corpus_rank":null,"citation_count":4,"citer_count":0,"citers_with_citation_signal":0,"citers_with_endowment":0,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":null,"is_data_producer":false,"deposit_databanks":null,"is_oa":false,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":null,"fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":1582988,"name":"Roberto Salmaso","orcid":null,"position":1,"is_corresponding":false},{"id":425756,"name":"Elena Fontana","orcid":"0000-0001-8853-3335","position":2,"is_corresponding":false},{"id":1516217,"name":"Anna Belloni Fortina","orcid":"0000-0001-5791-0775","position":3,"is_corresponding":false},{"id":1516216,"name":"Francesca Caroppo","orcid":"0000-0003-3583-0816","position":0,"is_corresponding":false}],"reference_count":0,"raw_metadata":{"has_enrichment":true,"resolved":true,"title":"A case of congenital dermatofibrosarcoma protuberans in a 2-year-old child","abstract":"Dermatofibrosarcoma protuberans is a rare cutaneous soft tissue tumor with a limited potential for metastasis, but a high risk of invasive growth and local recurrence. It is histologically characterized by a dense proliferation of uniform monomorphic spindle cells in the dermis, often infiltrating subcutaneous tissues (fat, muscle, and even bone). Fibroblasts appear arranged in disorganized fascicles with a typical storiform pattern within a slightly myxoid stroma. Tumor cells of dermatofibrosarcoma protuberans usually are positive for CD34 and negative for protein S100 and factor XIIIa.","is_dataset_classified":null,"base_score":1.6094379124341003,"endowment":1.6094379124341003,"datacite_reuse_total":0,"file_count":0,"downloads":0,"views":0,"has_version_chain":false,"is_dataset":false,"is_oa":false,"pmid":"32613051","pmcid":"PMC7317163","openalex_id":"https://openalex.org/W3025432356","authors":[],"funders":[],"total_grants":0,"fwci":0.0,"citation_percentile":0.06987829,"influential_citations":0,"citation_trend":[{"year":2024,"count":1},{"year":2025,"count":1},{"year":2026,"count":2}],"oa_status":"gold","license":"cc-by","oa_locations":[{"url":"http://www.jaadcasereports.org/article/S2352512620303684/pdf","host_type":"journal"},{"url":"http://www.jaadcasereports.org/article/S2352512620303684/pdf","host_type":"publisher"},{"url":"https://api.elsevier.com/content/article/PII:S2352512620303684?httpAccept=text/xml","host_type":"publisher"},{"url":"https://api.elsevier.com/content/article/PII:S2352512620303684?httpAccept=text/plain","host_type":"publisher"},{"url":"https://doi.org/10.1016/j.jdcr.2020.05.015","host_type":"journal"},{"url":"https://pubmed.ncbi.nlm.nih.gov/32613051","host_type":"repository"},{"url":"https://doaj.org/article/1b7c5c1e74734300963fcae6ace5acad","host_type":"repository"},{"url":"https://www.ncbi.nlm.nih.gov/pmc/articles/7317163","host_type":"repository"},{"url":"http://hdl.handle.net/11577/3378149","host_type":"repository"},{"url":"https://europepmc.org/articles/PMC7317163","host_type":"Europe_PMC"},{"url":"https://europepmc.org/articles/PMC7317163?pdf=render","host_type":"Europe_PMC"}],"fields_of_study":["Sarcoma Diagnosis and Treatment","Vascular Malformations and Hemangiomas","Tumors and Oncological Cases"],"mesh_terms":[],"keywords":["Dermatofibrosarcoma protuberans","Dermis","CD34","Medicine","Factor XIIIa","Pathology","Soft tissue","Stroma","Dermatofibrosarcoma","Metastasis","Immunohistochemistry","Biology","Cancer","Stem cell","Internal medicine"],"sdg_mappings":[{"sdg_number":0,"sdg_label":"Good health and well-being"}],"linked_datasets":[],"clinical_trials":[],"software_tools":[],"database_accessions":[],"source":"live","citation_network_status":"fetched"},"created_at":"2026-08-02T12:25:10.434825Z","pmid":null,"pmcid":null,"fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}