{"doi":"10.1016/j.jacc.2013.10.029","title":"Updated Clinical Classification of Pulmonary Hypertension","abstract":null,"journal":"Journal of the American College of Cardiology","year":2013,"id":672780,"datarank":1.251497382210742,"base_score":8.343315881404946,"endowment":8.343315881404946,"self_citation_contribution":1.251497382210742,"citation_network_contribution":0.0,"self_endowment_contribution":1.251497382210742,"citer_contribution":0.0,"corpus_percentile":null,"corpus_rank":null,"citation_count":4201,"citer_count":0,"citers_with_citation_signal":0,"citers_with_endowment":0,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":null,"is_data_producer":false,"deposit_databanks":null,"is_oa":false,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":null,"fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":1757841,"name":"Michael A. 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The main change was to withdraw persistent pulmonary hypertension of the newborn (PPHN) from Group 1 because this entity carries more differences than similarities with other PAH subgroups. In the current classification, PPHN is now designated number 1. Pulmonary hypertension associated with chronic hemolytic anemia has been moved from Group 1 PAH to Group 5, unclear/multifactorial mechanism. In addition, it was decided to add specific items related to pediatric pulmonary hypertension in order to create a comprehensive, common classification for both adults and children. Therefore, congenital or acquired left-heart inflow/outflow obstructive lesions and congenital cardiomyopathies have been added to Group 2, and segmental pulmonary hypertension has been added to Group 5. 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