{"doi":"10.1016/j.ajoc.2020.100640","title":"Spectrum of peripheral retinal ischemia in Wyburn-Mason syndrome","abstract":"PURPOSE: We report two cases of Wyburn-Mason syndrome that illustrate the spectrum of peripheral retinal ischemia seen in this condition. OBSERVATIONS: A 12-year-old female presented with a retinal arteriovenous malformation and sclerotic vessels associated with retinal ischemia on fluorescein angiography, as well as an ipsilateral ophthalmic arteriovenous malformation on magnetic resonance imaging. An 11-year-old male presented with retinal vascular engorgement and tortuosity along with a central retinal vein occlusion and secondary neovascularization. CONCLUSIONS AND IMPORTANCE: Retinal ischemia in Wyburn-Mason syndrome is heterogeneous and may be progressive, with secondary complications that result in neovascularization. Furthermore, it is necessary to recognize that this is a systemic condition that requires neurological evaluation.","journal":"American Journal of Ophthalmology Case Reports","year":2020,"id":109932,"datarank":0.3521255616933493,"base_score":2.0794415416798357,"endowment":2.0794415416798357,"self_citation_contribution":0.31191623125197543,"citation_network_contribution":0.04020933044137387,"self_endowment_contribution":0.31191623125197543,"citer_contribution":0.04020933044137387,"corpus_percentile":null,"corpus_rank":null,"citation_count":7,"citer_count":7,"citers_with_citation_signal":3,"citers_with_endowment":3,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":0.9551,"is_data_producer":false,"deposit_databanks":null,"is_oa":true,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":"2020-01-01","fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":395939,"name":"James Lin","orcid":"0000-0002-4520-9591","position":1,"is_corresponding":false},{"id":454928,"name":"Supalert Prakhunhungsit","orcid":"0000-0002-0211-113X","position":2,"is_corresponding":false},{"id":430632,"name":"Carlos E. Mendoza‐Santiesteban","orcid":"0000-0002-6344-4544","position":3,"is_corresponding":false},{"id":309188,"name":"Audina M. Berrocal","orcid":"0000-0002-2446-2184","position":4,"is_corresponding":false},{"id":523944,"name":"Blake H. Fortes","orcid":"0000-0002-3206-0062","position":0,"is_corresponding":true}],"reference_count":16,"raw_metadata":{"citation_network_status":"fetched"},"created_at":"2026-07-18T23:12:54.309019Z","pmid":"32181415","pmcid":null,"fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}