{"doi":"10.1002/jpn3.12443","title":"Determining the time to cholangiocarcinoma in pediatric‐onset PSC‐IBD","abstract":"Primary sclerosing cholangitis (PSC) is a risk factor for cholangiocarcinoma. When a child is diagnosed with both PSC and inflammatory bowel disease (IBD), evidence-based information on counseling families and risk management of developing cholangiocarcinoma is limited. In this case series (PubMed/collaborators), we included patients with PSC-IBD who developed cholangiocarcinoma and contacted authors to determine an event curve specifying the time between the second diagnosis (IBD or PSC) and a diagnosis of cholangiocarcinoma. Review of n = 175 studies resulted in a cohort of n = 21 patients with pediatric-onset PSC-IBD-cholangiocarcinoma. The median time to development of cholangiocarcinoma was 6.95 years from the second diagnosis. Despite the small number, 38% of cholangiocarcinoma developed within the first 2 years, and 47% of patients developed cholangiocarcinoma in the transition period to adult care (age 14-25). Our findings highlight the importance of screening that extends over the so-called transition period from pediatric to adult care.","journal":"Journal of Pediatric Gastroenterology and Nutrition","year":2024,"id":470227,"datarank":0.0,"base_score":0.0,"endowment":0.0,"self_citation_contribution":0.0,"citation_network_contribution":0.0,"self_endowment_contribution":0.0,"citer_contribution":0.0,"corpus_percentile":null,"corpus_rank":null,"citation_count":3,"citer_count":0,"citers_with_citation_signal":0,"citers_with_endowment":0,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":0.955,"is_data_producer":false,"deposit_databanks":null,"is_oa":true,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":"2024-01-01","fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":1304271,"name":"Johan Fevery","orcid":"0000-0002-7565-8726","position":1,"is_corresponding":false},{"id":991884,"name":"Douglas G. Adler","orcid":"0000-0003-3214-6285","position":2,"is_corresponding":false},{"id":1055306,"name":"Annika Bergquist","orcid":"0000-0002-3858-6241","position":3,"is_corresponding":false},{"id":1049430,"name":"Lissy de Ridder","orcid":"0000-0002-6035-1182","position":4,"is_corresponding":false},{"id":286707,"name":"Mark Deneau","orcid":"0000-0003-0459-9404","position":5,"is_corresponding":false},{"id":1304272,"name":"Corinne Gower‐Rousseau","orcid":"0000-0002-3925-5364","position":6,"is_corresponding":false},{"id":1304273,"name":"Roger W. Chapman","orcid":"0000-0001-9147-2852","position":7,"is_corresponding":false},{"id":1304274,"name":"Kate D. Lynch","orcid":"0000-0001-7748-2165","position":8,"is_corresponding":false},{"id":1304699,"name":"Catherine A. Stedman","orcid":null,"position":9,"is_corresponding":false},{"id":1049431,"name":"David C. Wilson","orcid":"0000-0003-0879-1129","position":10,"is_corresponding":false},{"id":286725,"name":"Uzma Shah","orcid":"0000-0003-0671-0639","position":11,"is_corresponding":false},{"id":258715,"name":"Lipika Goyal","orcid":"0000-0002-9777-6221","position":12,"is_corresponding":false},{"id":1304275,"name":"Harland S. Winter","orcid":"0000-0002-3202-7772","position":13,"is_corresponding":false},{"id":108261,"name":"Jochen K. Lennerz","orcid":"0000-0003-2434-4978","position":14,"is_corresponding":false},{"id":1304270,"name":"Batul Kaj‐Carbaidwala","orcid":"0000-0001-6045-9559","position":0,"is_corresponding":true}],"reference_count":16,"raw_metadata":null,"created_at":"2026-07-19T02:05:36.656771Z","pmid":"39704261","pmcid":null,"fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}