{"doi":"10.1002/hed.27546","title":"<scp>RANK‐L</scp> inhibitor as a promising agent for refractory extensive craniofacial fibrous dysplasia: A case report","abstract":"BACKGROUND: McCune-Albright syndrome is a rare disorder characterized by polyostotic fibrous dysplasia (FD), café-au-lait skin pigmentation, and endocrine dysfunction. Extensive FD in the craniofacial region can present significant challenges in terms of disease control and carries a high risk of permanent visual impairment. METHODS: We present a case of medically and surgically resistant FD that required nine optic nerve decompressions. RESULTS: The condition was ultimately controlled with the use of the denosumab agent. CONCLUSION: The case highlights the importance and potential efficacy of denosumab in resistant FD management, particularly in cases involving sensitive organs.","journal":"Head & Neck","year":2023,"id":375742,"datarank":0.0,"base_score":0.0,"endowment":0.0,"self_citation_contribution":0.0,"citation_network_contribution":0.0,"self_endowment_contribution":0.0,"citer_contribution":0.0,"corpus_percentile":null,"corpus_rank":null,"citation_count":4,"citer_count":0,"citers_with_citation_signal":0,"citers_with_endowment":0,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":0.9591,"is_data_producer":false,"deposit_databanks":null,"is_oa":true,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":"2023-01-01","fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":1138249,"name":"Mohammad Bilal Alsavaf","orcid":"0000-0002-6722-2244","position":1,"is_corresponding":false},{"id":757272,"name":"Daniel M. Prevedello","orcid":"0000-0003-0214-2339","position":2,"is_corresponding":false},{"id":1138250,"name":"Luma Ghalib","orcid":"0000-0003-0077-0665","position":3,"is_corresponding":false},{"id":335188,"name":"Alison M. Boyce","orcid":"0000-0002-2725-2908","position":4,"is_corresponding":false},{"id":757273,"name":"Ricardo L. Carrau","orcid":"0000-0003-3867-2032","position":5,"is_corresponding":false},{"id":1138248,"name":"Moataz D. Abouammo","orcid":"0000-0001-6970-1874","position":0,"is_corresponding":true}],"reference_count":7,"raw_metadata":null,"created_at":"2026-07-19T01:16:23.381203Z","pmid":"37823398","pmcid":null,"fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}