{"doi":"10.1002/dad2.12148","title":"Uniform data set language measures for bvFTD and PPA diagnosis and monitoring","abstract":"INTRODUCTION: The Frontotemporal Lobar Degeneration Module (FTLD-MOD) includes a neuropsychological battery designed to assess the clinical features of FTLD, although much is unknown about its utility. We investigated FTLD-MOD and Uniform Data Set 3.0 (UDS) language tests for differential diagnosis and disease monitoring. METHODS: Linear regressions compared baseline performances in 1655 National Alzheimer's Coordinating Center participants (behavioral variant frontotemporal dementia (bvFTD, n = 612), semantic variant primary progressive aphasia (svPPA, n = 168), non-fluent/agrammatic variant PPA (nfvPPA, n = 168), logopenic variant PPA (lvPPA, n = 109), and controls (n = 581)). Sample sizes to detect treatment effects were estimated using longitudinal data. RESULTS: Among PPAs, the FTLD-MOD language tasks and UDS Multilingual Naming Test accurately discriminated svPPA. Number Span Forward best discriminated lvPPA; Phonemic:Semantic Fluency ratio was excellent for nfvPPA classification. UDS fluency and naming measures required the smallest sample size to detect meaningful change. DISCUSSION: The FTLD-MOD and UDS differentiated among PPA subtypes. UDS 3.0 measures performed best for longitudinal monitoring.","journal":"Alzheimer s & Dementia Diagnosis Assessment & Disease Monitoring","year":2021,"id":168394,"datarank":0.8891720527369454,"base_score":3.4339872044851463,"endowment":3.4339872044851463,"self_citation_contribution":0.515098080672772,"citation_network_contribution":0.3740739720641735,"self_endowment_contribution":0.515098080672772,"citer_contribution":0.3740739720641735,"corpus_percentile":77.28784714164152,"corpus_rank":2937,"citation_count":30,"citer_count":17,"citers_with_citation_signal":14,"citers_with_endowment":14,"datacite_reuse_total":0,"is_dataset":true,"is_dataset_confidence":0.8315,"is_data_producer":false,"deposit_databanks":null,"is_oa":true,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":"2021-01-01","fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":49969,"name":"Sandra Weıntraub","orcid":"0000-0003-2605-5205","position":1,"is_corresponding":false},{"id":256795,"name":"Katya Rascovsky","orcid":null,"position":2,"is_corresponding":false},{"id":270253,"name":"Katherine P. Rankin","orcid":"0000-0002-3611-0848","position":3,"is_corresponding":false},{"id":227724,"name":"Jack C. Taylor","orcid":"0000-0002-6431-9956","position":4,"is_corresponding":false},{"id":253904,"name":"Julie A. Fields","orcid":"0000-0002-1282-9866","position":5,"is_corresponding":false},{"id":329465,"name":"Kaitlin B. Casaletto","orcid":"0000-0001-5000-7604","position":6,"is_corresponding":false},{"id":309226,"name":"Argye E. Hillis","orcid":"0000-0002-5192-1171","position":7,"is_corresponding":false},{"id":351163,"name":"Sladjana Lukic","orcid":"0000-0001-7009-3474","position":8,"is_corresponding":false},{"id":260467,"name":"Maria Luisa Gorno‐Tempini","orcid":"0000-0002-7426-7782","position":9,"is_corresponding":false},{"id":253906,"name":"Hilary W. Heuer","orcid":"0000-0002-3776-1685","position":10,"is_corresponding":false},{"id":248198,"name":"Merilee Teylan","orcid":null,"position":11,"is_corresponding":false},{"id":253925,"name":"Walter A. Kukull","orcid":"0000-0001-8761-9014","position":12,"is_corresponding":false},{"id":58513,"name":"Bruce L. Miller","orcid":"0000-0002-2152-4220","position":13,"is_corresponding":false},{"id":108587,"name":"Bradley F. Boeve","orcid":"0000-0002-4153-8187","position":14,"is_corresponding":false},{"id":230946,"name":"Howard J. Rosen","orcid":"0000-0001-9281-7402","position":15,"is_corresponding":false},{"id":253908,"name":"Adam L. Boxer","orcid":"0000-0002-1215-5064","position":16,"is_corresponding":false},{"id":253924,"name":"Joel H. Kramer","orcid":"0000-0002-2917-8297","position":17,"is_corresponding":false},{"id":260464,"name":"Adam M. Staffaroni","orcid":"0000-0002-3903-9805","position":0,"is_corresponding":true}],"reference_count":52,"raw_metadata":null,"created_at":"2026-07-18T23:46:06.853307Z","pmid":"33665340","pmcid":"PMC7896637","fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}