{"doi":"10.1002/ana.26549","title":"Cerebral Cortical Encephalitis in Myelin Oligodendrocyte Glycoprotein Antibody‐Associated Disease","abstract":"Cerebral cortical encephalitis (CCE) is a recently described myelin oligodendrocyte glycoprotein antibody-associated disease (MOGAD) phenotype. In this observational retrospective study, we characterized 19 CCE patients (6.7% of our MOGAD cohort). Headache (n = 15, 79%), seizures (n = 13, 68%), and encephalopathy (n = 12, 63%) were frequent. Magnetic resonance imaging revealed unilateral (n = 12, 63%) or bilateral (n = 7, 37%) cortical T2 hyperintensity and leptomeningeal enhancement (n = 17, 89%). N-Methyl-D-aspartate receptor autoantibodies coexisted in 2 of 15 tested (13%). CCE pathology (n = 2) showed extensive subpial cortical demyelination (n = 2), microglial reactivity (n = 2), and inflammatory infiltrates (perivascular, n = 1; meningeal, n = 1). Most received high-dose steroids (n = 17, 89%), and all improved, but 3 had CCE relapses. This study highlights the CCE spectrum and provides insight into its pathogenesis. ANN NEUROL 2023;93:297-302.","journal":"Annals of Neurology","year":2022,"id":235541,"datarank":0.0,"base_score":0.0,"endowment":0.0,"self_citation_contribution":0.0,"citation_network_contribution":0.0,"self_endowment_contribution":0.0,"citer_contribution":0.0,"corpus_percentile":null,"corpus_rank":null,"citation_count":79,"citer_count":0,"citers_with_citation_signal":0,"citers_with_endowment":0,"datacite_reuse_total":0,"is_dataset":false,"is_dataset_confidence":0.9425,"is_data_producer":false,"deposit_databanks":null,"is_oa":true,"file_count":0,"downloads":0,"has_version_chain":false,"published_date":"2022-01-01","fair_score":null,"fair_percentile":null,"algorithm_id":"datarank_citation_only_1hop_v6","ranking_scope":"data_only","authors":[{"id":586755,"name":"Yong Guo","orcid":"0009-0003-4462-750X","position":1,"is_corresponding":false},{"id":414058,"name":"Karl N. Krecke","orcid":"0000-0003-1950-5589","position":2,"is_corresponding":false},{"id":286579,"name":"John J. Chen","orcid":"0000-0003-3644-7528","position":3,"is_corresponding":false},{"id":761762,"name":"Vyanka Redenbaugh","orcid":"0000-0001-6400-7760","position":4,"is_corresponding":false},{"id":854266,"name":"Mayra Montalvo","orcid":"0000-0003-1386-9998","position":5,"is_corresponding":false},{"id":854267,"name":"Paul Elsbernd","orcid":"0000-0001-7572-3615","position":6,"is_corresponding":false},{"id":252994,"name":"Jan‐Mendelt Tillema","orcid":null,"position":7,"is_corresponding":false},{"id":231251,"name":"A. Sebastian López‐Chiriboga","orcid":"0000-0001-5653-5600","position":8,"is_corresponding":false},{"id":854268,"name":"Adrian Budhram","orcid":"0000-0003-4860-0470","position":9,"is_corresponding":false},{"id":369544,"name":"Elia Sechi","orcid":"0000-0003-4698-663X","position":10,"is_corresponding":false},{"id":286576,"name":"Amy Kunchok","orcid":"0000-0002-8387-6491","position":11,"is_corresponding":false},{"id":854269,"name":"Divyanshu Dubey","orcid":"0000-0002-4302-4075","position":12,"is_corresponding":false},{"id":231254,"name":"Sean J. Pittock","orcid":"0000-0002-6140-5584","position":13,"is_corresponding":false},{"id":231257,"name":"Claudia F. Lucchinetti","orcid":"0000-0001-5070-1196","position":14,"is_corresponding":false},{"id":231250,"name":"Eoin P. Flanagan","orcid":"0000-0002-6661-2910","position":0,"is_corresponding":true}],"reference_count":20,"raw_metadata":null,"created_at":"2026-07-19T00:21:53.333008Z","pmid":"36372941","pmcid":null,"fwci":null,"citation_percentile":null,"influential_citations":0,"oa_status":null,"license":null,"views":0,"total_file_size_bytes":0,"version_count":0,"fair_f":null,"fair_a":null,"fair_i":null,"fair_r":null,"fair_zscore":null,"fair_rationale":null,"fair_model":null,"fair_agent_version":null,"fair_fulltext_source":null,"fair_has_llm":null,"fair_computed_at":null,"clinical_trials":[],"software_tools":[],"db_accessions":[],"linked_datasets":[],"topics":[]}